tumorsMalignant tumoursMalignant tumours2224-50572587-6813Rosoncoweb10.18027/2224-5057-2025-052tumors-1496Research ArticleКЛИНИЧЕСКИЕ СЛУЧАИCLINICAL NOTESЭпителиоидная гемангиоэндотелиома лёгкого: клинический случайEpithelioid hemangioendothelioma of the lung: a clinical casehttps://orcid.org/0009-0008-4164-2372ТуромшаА. Н.TuromshaA. N.

Алеся Николаевна Туромша 

197372 Санкт-Петербург, ул. Ильюшина, 4 / 1 

Alesya Nikolaevna Turomsha

4/1 Ilyushina St., Saint Petersburg 197372

turomsha-an@avaclinic.ruhttps://orcid.org/0000-0001-7930-8048ПротасоваА. Э.ProtasovaA. E.

Анна Эдуардовна Протасова 

197372 Санкт-Петербург, ул. Ильюшина, 4 / 1 

197341 СанктПетербург, ул. Аккуратова, 2 

199034 Санкт-Петербург, Университетская набережная, 7–9 

Anna Eduardovna Protasova

4/1 Ilyushina St., Saint Petersburg 197372

2 Akkuratova St., Saint Petersburg 197341

7-9 Universitetskaya Emb., Saint Petersburg 19903

https://orcid.org/0009-0008-4392-0700ШереметМ. Ю.SheremetM. Yu.

Марина Юрьевна Шеремет 

197372 Санкт-Петербург, ул. Ильюшина, 4 / 1

Marina Yurevna Sheremet

4/1 Ilyushina St., Saint Petersburg 197372

ООО «АВА-ПЕТЕР»РоссияAVA-PBTBR LLCRussian FederationООО «АВА-ПЕТЕР» ; ФГБУ «Национальный медицинский исследовательский центр им. В. А. Алмазова» Минздрава России ; ФБОУ ВО «Санкт-Петербургский государственный университет»РоссияAVA-PBTBR LLC ; V. A. Almazov National Medical Research Centre, Ministry of Health of Russia ; Saint Petersburg State UniversityRussian Federation2025301020251536167Copyright © Туромша А.Н., Протасова А.Э., Шеремет М.Ю., 20252025Туромша А.Н., Протасова А.Э., Шеремет М.Ю.Turomsha A.N., Protasova A.E., Sheremet M.Y.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.malignanttumors.org/jour/article/view/1496

Эпителиоидная гемангиоэндотелиома (ЭГЭ) — крайне редкая сосудистая саркома, характеризующаяся уникальными морфологическими и молекулярными признаками. Заболеваемость составляет около 1 случая на миллион человек. В данной публикации представлены данные клинических случаев с различными локализациями ЭГЭ, опубликованных в отечественной литературе. Представлен наш уникальный клинический пример ЭГЭ лёгкого, сопровождавшийся значительными трудностями гистологической верификации. В работе проанализированы особенности диагностики данного заболевания, а также представлены данные о проведённом лечении и его результатах.

Epithelioid hemangioendothelioma (EGE) is an extremely rare vascular sarcoma characterized by unique morpho­logical and molecular features. The incidence is about 1 case per million people. This publication presents data on clinical cases with various localizations of EGE published in the Russian literature. Our unique clinical example of lung EGE is presented, which was accompanied by significant difficulties in histological verification. The paper analyzes the features of the diagnosis of this disease, as well as presents data on the treatment and its results.

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The authors declare that there are no conflicts of interest present.